Chinese Journal of Evidence -Based Pediatric ›› 2020, Vol. 15 ›› Issue (5): 365-369.

• Original Papers • Previous Articles     Next Articles

Prenatal echocardiographic features of anatomically corrected malposition of the great arteries {S,D,L}

LI Wenxiu1,3, FANG Haiyan2,3, GENG Bin1, YANG Shuang1 , WU Jiang1   

  1. 1 Pediatric Cardiovascular Center, Beijing Anzhen Hospital Affiliated to the Capital Medical University, Beijing 100029, China;2 Ultrasound Department, the First Affiliated Hospital of Jinan University, Guangzhou 510630, China; 3 Co-first author  
  • Received:2020-09-07 Revised:2020-10-03 Online:2020-10-25 Published:2020-10-25
  • Contact: GENG Bin

Abstract: ObjectiveTo analyze the prenatal echocardiographic features of anatomically corrected malposition of the great arteries (ACMGA) {S,D,L} in order to improve the prenatal diagnosis accuracy. MethodsFetal echocardiographic features were retrospectively analyzed with prenatal diagnosis of ACMGA {S,D,L} at Beijing Anzhen Hospital between November 2016 and August 2020, and the fetal echocardiography characteristics of ACMGA {S,D,L} and the key points of its identification were summarized. ResultsThere were 5 fetuses with ACMGA. The age of pregnant women was 26 to 35 (29.4±3.6) years old, and the pregnancy period was 23 to 28 (24.2±2.2) weeks. Four cases had induced labor including 1 case of diagnosis confirmation by postmortem examination. One case was confirmed by echocardiography, cardiac CT and surgery (pulmonary artery banding) after birth. Echocardiographic features included: a. The viscera and atria were in situs solitus, the type of ventricular loop was d-loop and atrioventricular connections was normal. b. The aorta originated above the left ventricle, the pulmonary artery originated above the anatomically right ventricle and their proximal segments were parallel to each other. c. The spatial relationship between the arota and pulmonary artery was abnormal and the aorta was to the left of the pulmonary artery. d. The muscular conus (subaortic and/or subpulmonary) was showed between the two arteries. e. A muscular subaortic conus separated the aortic and mitral valves. f. There was always no muscular subpulmonary conus between pulmonary valve and tricuspid valve. g. The left ventricular outflow tract was longer and the shape was like "swan neck". h. This malformation was usually associated with ventricular septal defect (VSD), bilateral atrial appendage juxtaposition, persistent left superior venacava (PLSVC), and other intracardiac malformations. ConclusionThe Van Praagh segmental analysis principle should be strictly followed during the scan to determine the anatomical status of each cardiac segment. The differential diagnosis of ACMGA {S,D,L} is mainly with the double outlet right ventricular (DORV).